Rituximab therapy in nephrotic syndrome due to AH amyloidosis.
نویسندگان
چکیده
We report a patient with AH amyloidosis associated with lymphoplasmacytic leukemia that has remained in a stable state with a nephrotic syndrome for 17 months since the commencement of cyclic rituximab therapy aimed at suppression of pathogenetic gamma heavy chains. Free light chains in serum and CD20-positive cells in peripheral blood were useful as hematological markers in the patient. Rituximab might be a potent therapeutic option for AH amyloidosis associated with a B-cell lymphoproliferative disorder.
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عنوان ژورنال:
- Amyloid : the international journal of experimental and clinical investigation : the official journal of the International Society of Amyloidosis
دوره 16 3 شماره
صفحات -
تاریخ انتشار 2009